Vasculitis of the peripheral nervous system

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1 4 rd Congress of the European Academy of Neurology Lisbon, Portugal, June 16-19, 2018 Teaching Course 5 Acute emergencies in neuromuscular disease - Level 2 Vasculitis of the peripheral nervous system Alexander Vrancken Utrecht, The Netherlands A.F.J.E.vrancken@umcutrecht.nl

2 Conflict of interest: The author has no conflict of interest in relation to this manuscript 1

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13 References: Agadi JB et al. Usefulness of superficial peroneal nerve/peroneus brevis muscle biopsy in the diagnosis of vasculitic neuropathy. J Clin Neurosci. 2012;19(10): Anish L et al, Neuropathy in elderly: lessons learnt from nerve biopsy. Age Ageing. 2015;44(2): Berti A et al. The epidemiology of antineutrophil cytoplasmic autoantibodyassociated vasculitis in Olmsted county, Minnesota: a twenty-year US population-based study. Arthritis Rheumatol. 2017;69(12): Chen DJ, Prayson RA. Evaluation of simultaneous muscle and nerve biopsies for the diagnosis of neuromuscular diseases. Ann Diagn Pathol. 2014;18(5): Chia L et al. Contribution of nerve biopsy findings to the diagnosis of disabling neuropathy in the elderly. A retrospective review of 100 consecutive patients. Brain. 1996;119 (Pt4): Cho HJ et al. Clinical characteristics and treatment response of peripheral neuropathy in the presence of eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome): experience at a single tertiary center. J Clin Neurol. 2017;13(1): Collins MP, Hadden RD. The nonsystemic vasculitic neuropathies. Nat Rev Neurol. 2017;13(5): Collins MP et al. Peripheral Nerve Society Guideline on the classification, diagnosis, investigation, and immunosuppressive therapy of non-systemic vasculitic neuropathy: executive summary. J Peripher Nerv Syst. 2010;15(3): Duchesne M et al. Value of nerve biopsy in patients with latent malignant hemopathy and peripheral neuropathy: a case series. Medicine 2015 Jan;94(3):e394. Gwathmey KG et al. Vasculitic neuropathies. Lancet Neurol. 2014;13(1): Hadden RDM et al. Vasculitic peripheral neuropathy: case definition and guidelines for collection, analysis, and presentation of immunisation safety data. Vaccine. 2017;35(11): Jennette JC. Overview of the 2012 revised International Chapel Hill Consensus Conference nomenclature of vasculitides. Clin Exp Nephrol. 2013;17(5): Kararizou E et al. Polyneuropathies in the elderly: a clinico pathological study of 74 cases. Int J Neurosci May;116(5): Koike H et al. Intravenous immunoglobulin for chronic residual peripheral neuropathy in eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome): a multicenter, double-blind trial. J Neurol. 2015;262(3): Kurt S et al. Aymptomatic vasculitic neuropathy. Muscle Nerve 2015;52(1):

14 McCluskey L et al. "Pseudo-conduction block" in vasculitic neuropathy. Muscle Nerve 1999;22(10): Mohammad AJ et al. Incidence and survival rates in Wegener's granulomatosis, microscopic polyangiitis, Churg-Strauss syndrome and polyarteritis nodosa. Rheumatology 2009;48(12): Myasoedova E et al. Incidence of extraarticular rheumatoid arthritis in Olmsted County, Minnesota, in versus : a populationbased study. J Rheumatol. 2011;38(6): Nesher G et al. The incidence of primary systemic vasculitis in Jerusalem: a 20-year hospital-based retrospective study. J Rheumatol. 2016;43(6): Ntatsaki E et al. Systemic rheumatoid vasculitis in the era of modern immunosuppressive therapy. Rheumatology 2014;53(1): Said G et al. Nerve granulomas and vasculitis in sarcoid peripheral neuropathy: a clinicopathological study of 11 patients. Brain 2002;125(Pt 2): Samson M et al. Mononeuritis multiplex predicts the need for immunosuppressive or immunomodulatory drugs for EGPA, PAN and MPA patients without poor-prognosis factors. Autoimmun Rev. 2014;13(9): Suppiah R et al. Peripheral neuropathy in ANCA-associated vasculitis: outcomes from the European Vasculitis Study Group trials. Rheumatology 2011;50(12): Tracy JA et al. Primary amyloidosis presenting as upper limb multiple mononeuropathies. Muscle Nerve. 2010;41(5): Vital C et al. Usefulness of combined nerve and muscle biopsy in the diagnosis of amyloid neuropathy--a study of 6 new cases. Clin Neuropathol. 2010;29(2): Vital C et al. Combined nerve and muscle biopsy in the diagnosis of vasculitic neuropathy. A 16-year retrospective study of 202 cases. J Peripher Nerv Syst. 2006;11(1):20-9. Vrancken AF, Said G. Vasculitic neuropathy. Handb Clin Neurol. 2013;115: Vrancken AF et al. The additional yield of combined nerve/muscle biopsy in vasculitic neuropathy. Eur J Neurol Jan;18(1): Vrancken AF et al. Immunosuppressive treatment for non-systemic vasculitic neuropathy. Cochrane Database Syst Rev. 2007;(1):CD Watts RA et al. Classification, epidemiology and clinical subgrouping of antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis. Nephrol Dial Transplant. 2015;30 Suppl 1:i Wolf J et al. Peripheral neuropathy as initial manifestation of primary systemic vasculitides. J Neurol. 2013;260(4): Üçeyler N et a. Non-systemic vasculitic neuropathy: single-center follow-up of 60 patients. J Neurol. 2015;262(9):

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