ERA-EDTA ERA-EDTA Primary Renal Diagnosis (PRD) Term ERA-EDTA PRD classification SNOMED CT PRD Code 1/1/2015

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1 1003 Adult nephrotic syndrome - no histology Immunological Glomerulopathy Nephrotic syndrome of childhood - steroid sensitive - no histology Immunological Glomerulopathy Congenital nephrotic syndrome (CNS) - no histology Immunological Glomerulopathy Congenital nephrotic syndrome (CNS) - Finnish type - no histology Immunological Glomerulopathy Congenital nephrotic syndrome (CNS) - Finnish type - histologically proven Immunological Glomerulopathy Congenital nephrotic syndrome (CNS) - diffuse mesangial sclerosis Immunological Glomerulopathy Congenital nephrotic syndrome (CNS) - focal segmental glomerulosclerosis (FSGS) Immunological Glomerulopathy Denys-Drash syndrome Immunological Glomerulopathy Congenital nephrotic syndrome (CNS) - congenital infection Immunological Glomerulopathy Minimal change nephropathy - no histology Immunological Glomerulopathy Minimal change nephropathy - histologically proven Immunological Glomerulopathy IgA nephropathy - no histology Immunological Glomerulopathy IgA nephropathy - histologically proven Immunological Glomerulopathy Familial IgA nephropathy - no histology Immunological Glomerulopathy Familial IgA nephropathy - histologically proven Immunological Glomerulopathy IgA nephropathy secondary to liver cirrhosis - no histology Immunological Glomerulopathy IgA nephropathy secondary to liver cirrhosis - histologically proven Immunological Glomerulopathy IgM - associated nephropathy Immunological Glomerulopathy Membranous nephropathy - idiopathic Immunological Glomerulopathy Membranous nephropathy - malignancy associated Immunological Glomerulopathy Membranous nephropathy - drug induced Immunological Glomerulopathy Membranous nephropathy - infection associated Immunological Glomerulopathy Mesangiocapillary glomerulonephritis type 1 Immunological Glomerulopathy Mesangiocapillary glomerulonephritis type 2 (dense deposit disease) Immunological Glomerulopathy Mesangiocapillary glomerulonephritis type 3 Immunological Glomerulopathy Idiopathic rapidly progressive (crescentic) glomerulonephritis Immunological Glomerulopathy Primary focal segmental glomerulosclerosis (FSGS) Immunological Glomerulopathy Focal segmental glomerulosclerosis (FSGS) secondary to obesity - no histology Immunological Glomerulopathy Focal segmental glomerulosclerosis (FSGS) secondary to obesity - histologically proven Immunological Glomerulopathy Diffuse endocapillary glomerulonephritis Immunological Glomerulopathy Mesangial proliferative glomerulonephritis Immunological Glomerulopathy Focal and segmental proliferative glomerulonephritis Immunological Glomerulopathy Glomerulonephritis - secondary to other systemic disease Immunological Glomerulopathy Glomerulonephritis - histologically indeterminate Immunological Glomerulopathy Systemic vasculitis - ANCA negative - histologically proven Immunological Glomerulopathy Systemic vasculitis - ANCA positive - no histology Immunological Glomerulopathy Granulomatosis with polyangiitis - no histology Immunological Glomerulopathy Granulomatosis with polyangiitis - histologically proven Immunological Glomerulopathy Microscopic polyangiitis - histologically proven Immunological Glomerulopathy Churg-Strauss syndrome - no histology Immunological Glomerulopathy Churg-Strauss syndrome - histologically proven Immunological Glomerulopathy Polyarteritis nodosa Immunological Glomerulopathy / 7

2 1464 Anti-Glomerular basement membrane (GBM) disease / Goodpasture's syndrome - no histology Immunological Glomerulopathy Anti-Glomerular basement membrane (GBM) disease / Goodpasture's syndrome - histologically proven Immunological Glomerulopathy Systemic lupus erythematosus / nephritis - no histology Immunological Glomerulopathy Systemic lupus erythematosus / nephritis - histologically proven Immunological Glomerulopathy Henoch-Schönlein purpura / nephritis - no histology Immunological Glomerulopathy Henoch-Schönlein purpura / nephritis - histologically proven Immunological Glomerulopathy Renal scleroderma / systemic sclerosis - no histology Immunological Glomerulopathy Renal scleroderma / systemic sclerosis - histologically proven Immunological Glomerulopathy Essential mixed cryoglobulinaemia - no histology Immunological Glomerulopathy Essential mixed cryoglobulinaemia - histologically proven Immunological Glomerulopathy Cryoglobulinaemia secondary to hepatitis C - no histology Immunological Glomerulopathy Cryoglobulinaemia secondary to hepatitis C - histologically proven Immunological Glomerulopathy Cryoglobulinaemia secondary to systemic disease - no histology Immunological Glomerulopathy Cryoglobulinaemia secondary to systemic disease - histologically proven Immunological Glomerulopathy Nephrotic syndrome of childhood - steroid resistant - no histology Immunological Glomerulopathy Nephrotic syndrome of childhood - no trial of steroids - no histology Immunological Glomerulopathy Glomerulonephritis - no histology Immunological Glomerulopathy Primary reflux nephropathy - sporadic Tubulo-Interstitial Disease Familial reflux nephropathy Tubulo-Interstitial Disease Congenital dysplasia / hypoplasia Tubulo-Interstitial Disease Multicystic dysplastic kidneys Tubulo-Interstitial Disease Dysplasia due to fetal ACE-inhibitor exposure Tubulo-Interstitial Disease Glomerulocystic disease Tubulo-Interstitial Disease Congenital pelvi-ureteric junction obstruction Tubulo-Interstitial Disease Congenital vesico-ureteric junction obstruction Tubulo-Interstitial Disease Posterior urethral valves Tubulo-Interstitial Disease Syndrome of agenesis of abdominal muscles - prune belly syndrome Tubulo-Interstitial Disease Congenital neurogenic bladder Tubulo-Interstitial Disease Bladder exstrophy Tubulo-Interstitial Disease Megacystis-megaureter Tubulo-Interstitial Disease Oligomeganephronia Tubulo-Interstitial Disease Renal papillary necrosis - cause unknown Tubulo-Interstitial Disease Acquired obstructive uropathy / nephropathy Tubulo-Interstitial Disease Acquired obstructive nephropathy due to neurogenic bladder Tubulo-Interstitial Disease Obstructive nephropathy due to prostatic hypertrophy Tubulo-Interstitial Disease Obstructive nephropathy due to prostate cancer Tubulo-Interstitial Disease Obstructive nephropathy due to bladder cancer Tubulo-Interstitial Disease Obstructive nephropathy due to other malignancies Tubulo-Interstitial Disease Idiopathic retroperitoneal fibrosis Tubulo-Interstitial Disease Retroperitoneal fibrosis secondary to malignancies Tubulo-Interstitial Disease Calculus nephropathy / urolithiasis Tubulo-Interstitial Disease Calcium oxalate urolithiasis Tubulo-Interstitial Disease / 7

3 1850 Enteric hyperoxaluria Tubulo-Interstitial Disease Magnesium ammonium phosphate (struvite) urolithiasis Tubulo-Interstitial Disease Uric acid urolithiasis Tubulo-Interstitial Disease Tubulointerstitial nephritis - no histology Tubulo-Interstitial Disease Tubulointerstitial nephritis - histologically proven Tubulo-Interstitial Disease Familial interstitial nephropathy - no histology Tubulo-Interstitial Disease Familial interstitial nephropathy - histologically proven Tubulo-Interstitial Disease Tubulointerstitial nephritis associated with autoimmune disease - no histology Tubulo-Interstitial Disease Tubulointerstitial nephritis associated with autoimmune disease - histologically proven Tubulo-Interstitial Disease Tubulointerstitial nephritis with uveitis (TINU) - no histology Tubulo-Interstitial Disease Tubulointerstitial nephritis with uveitis (TINU) - histologically proven Tubulo-Interstitial Disease Renal sarcoidosis - no histology Tubulo-Interstitial Disease Renal sarcoidosis - histologically proven Tubulo-Interstitial Disease Aristolochic acid nephropathy (Balkan / Chinese herb / endemic nephropathy) - no histology Tubulo-Interstitial Disease Aristolochic acid nephropathy (Balkan / Chinese herb / endemic nephropathy) - histologically proven Tubulo-Interstitial Disease Drug-induced tubulointerstitial nephritis - no histology Tubulo-Interstitial Disease Drug-induced tubulointerstitial nephritis - histologically proven Tubulo-Interstitial Disease Nephropathy due to analgesic drugs - no histology Tubulo-Interstitial Disease Nephropathy due to analgesic drugs - histologically proven Tubulo-Interstitial Disease Nephropathy due to ciclosporin - no histology Tubulo-Interstitial Disease Nephropathy due to ciclosporin - histologically proven Tubulo-Interstitial Disease Nephropathy due to tacrolimus - no histology Tubulo-Interstitial Disease Nephropathy due to tacrolimus - histologically proven Tubulo-Interstitial Disease Nephropathy due to aminoglycosides - no histology Tubulo-Interstitial Disease Nephropathy due to aminoglycosides - histologically proven Tubulo-Interstitial Disease Nephropathy due to amphotericin - no histology Tubulo-Interstitial Disease Nephropathy due to amphotericin - histologically proven Tubulo-Interstitial Disease Nephropathy due to cisplatin - no histology Tubulo-Interstitial Disease Nephropathy due to cisplatin - histologically proven Tubulo-Interstitial Disease Nephropathy due to lithium - no histology Tubulo-Interstitial Disease Nephropathy due to lithium - histologically proven Tubulo-Interstitial Disease Lead induced nephropathy - no histology Tubulo-Interstitial Disease Lead induced nephropathy - histologically proven Tubulo-Interstitial Disease Acute urate nephropathy - no histology Tubulo-Interstitial Disease Acute urate nephropathy - histologically proven Tubulo-Interstitial Disease Chronic urate nephropathy - histologically proven Tubulo-Interstitial Disease Radiation nephritis Tubulo-Interstitial Disease Renal / perinephric abscess Tubulo-Interstitial Disease OR Renal tuberculosis Tubulo-Interstitial Disease Leptospirosis Tubulo-Interstitial Disease Hantavirus nephropathy Tubulo-Interstitial Disease Xanthogranulomatous pyelonephritis Tubulo-Interstitial Disease / 7

4 2274 Nephropathy related to HIV - no histology Tubulo-Interstitial Disease Nephropathy related to HIV - histologically proven Tubulo-Interstitial Disease Schistosomiasis Tubulo-Interstitial Disease Other specific infection Tubulo-Interstitial Disease Renal cysts and diabetes syndrome Tubulo-Interstitial Disease Chronic urate nephropathy - no histology Tubulo-Interstitial Disease Hypercalcaemic nephropathy Tubulo-Interstitial Disease Retroperitoneal fibrosis secondary to peri-aortitis Tubulo-Interstitial Disease Retroperitoneal fibrosis secondary to drugs Tubulo-Interstitial Disease Diabetic nephropathy in type I diabetes - no histology Type 1 Diabetes Mellitus Diabetic nephropathy in type I diabetes - histologically proven Type 1 Diabetes Mellitus Diabetic nephropathy in type II diabetes - no histology Type 2 Diabetes Mellitus Diabetic nephropathy in type II diabetes - histologically proven Type 2 Diabetes Mellitus Chronic hypertensive nephropathy - no histology Vascular Disease Chronic hypertensive nephropathy - histologically proven Vascular Disease Malignant hypertensive nephropathy / accelerated hypertensive nephropathy - no histology Vascular Disease Malignant hypertensive nephropathy / accelerated hypertensive nephropathy - histologically proven Vascular Disease Ageing kidney - no histology Vascular Disease Ischaemic nephropathy - no histology Vascular Disease Ischaemic nephropathy / microvascular disease - histologically proven Vascular Disease Renal artery stenosis Vascular Disease Atheroembolic renal disease - no histology Vascular Disease Atheroembolic renal disease - histologically proven Vascular Disease Fibromuscular dysplasia of renal artery Vascular Disease Renal arterial thrombosis / occlusion Vascular Disease Renal vein thrombosis Vascular Disease Familial focal segmental glomerulosclerosis (FSGS) - autosomal recessive - no histology Hereditary Disease Familial focal segmental glomerulosclerosis (FSGS) - autosomal recessive - histologically proven Hereditary Disease Familial focal segmental glomerulosclerosis (FSGS) - autosomal dominant - no histology Hereditary Disease Familial focal segmental glomerulosclerosis (FSGS) - autosomal dominant - histologically proven Hereditary Disease Alport syndrome - no histology Hereditary Disease Alport syndrome - histologically proven Hereditary Disease Benign familial haematuria Hereditary Disease Thin basement membrane disease Hereditary Disease Medullary cystic kidney disease type I Hereditary Disease Medullary cystic kidney disease type II Hereditary Disease Uromodulin-associated nephropathy (familial juvenile hyperuricaemic nephropathy) Hereditary Disease Nephronophthisis Hereditary Disease Nephronophthisis - type 1 (juvenile type) Hereditary Disease Nephronophthisis - type 2 (infantile type) Hereditary Disease Nephronophthisis - type 3 (adolescent type) Hereditary Disease Nephronophthisis - type 4 (juvenile type) Hereditary Disease / 7

5 2889 Nephronophthisis - type 5 Hereditary Disease Nephronophthisis - type 6 Hereditary Disease Primary Fanconi syndrome Hereditary Disease Tubular disorder as part of inherited metabolic diseases Hereditary Disease Dent disease Hereditary Disease Lowe syndrome (oculocerebrorenal syndrome) Hereditary Disease Inherited aminoaciduria Hereditary Disease Cystinuria Hereditary Disease Cystinosis Hereditary Disease Inherited renal glycosuria Hereditary Disease Hypophosphataemic rickets X-linked (XL) Hereditary Disease Hypophosphataemic rickets autosomal recessive (AR) Hereditary Disease Primary renal tubular acidosis (RTA) Hereditary Disease Proximal renal tubular acidosis (RTA) - type II Hereditary Disease Distal renal tubular acidosis (RTA) - type I Hereditary Disease Distal renal tubular acidosis with sensorineural deafness - gene mutations Hereditary Disease Nephrogenic diabetes insipidus Hereditary Disease Lesch Nyhan syndrome - hypoxanthine guanine phosphoribosyl transferase deficiency Hereditary Disease Phosphoribosyl pyrophosphate synthetase (PRPPS) superactivity Hereditary Disease Alagille syndrome Hereditary Disease Bartter syndrome Hereditary Disease Gitelman syndrome Hereditary Disease Liddle syndrome Hereditary Disease Apparent mineralocorticoid excess Hereditary Disease Glucocorticoid suppressible hyperaldosteronism Hereditary Disease Inherited / genetic diabetes mellitus type II Hereditary Disease Pseudohypoaldosteronism type 1 Hereditary Disease Pseudohypoaldosteronism type 2 (Gordon syndrome) Hereditary Disease Familial hypocalciuric hypercalcaemia Hereditary Disease Familial hypercalciuric hypocalcaemia Hereditary Disease Familial hypomagnesaemia Hereditary Disease Primary hyperoxaluria Hereditary Disease Primary hyperoxaluria type I Hereditary Disease Primary hyperoxaluria type II Hereditary Disease Fabry disease - no histology Hereditary Disease Fabry disease - histologically proven Hereditary Disease Xanthinuria Hereditary Disease Nail-patella syndrome Hereditary Disease Rubinstein-Taybi syndrome Hereditary Disease Tuberous sclerosis Hereditary Disease Von Hippel-Lindau disease Hereditary Disease Medullary sponge kidneys Hereditary Disease / 7

6 3305 Horse-shoe kidney Hereditary Disease Frasier syndrome Hereditary Disease Branchio-oto-renal syndrome Hereditary Disease Williams syndrome Hereditary Disease Townes-Brocks syndrome Hereditary Disease Lawrence-Moon-Biedl / Bardet-Biedl syndrome Hereditary Disease Mitochondrial cytopathy Hereditary Disease Familial nephropathy Hereditary Disease Renal coloboma syndrome Hereditary Disease Primary hyperoxaluria type III Hereditary Disease Autosomal dominant (AD) polycystic kidney disease Cystic Disease Autosomal dominant (AD) polycystic kidney disease type I Cystic Disease Autosomal dominant (AD) polycystic kidney disease type II Cystic Disease Autosomal recessive (AR) polycystic kidney disease Cystic Disease Cystic kidney disease Cystic Disease Hepatorenal syndrome Other Renal amyloidosis Other AA amyloid secondary to chronic inflammation Other AL amyloid secondary to plasma cell dyscrasia Other Familial amyloid secondary to protein mutations - no histology Other Familial amyloid secondary to protein mutations - histologically proven Other Familial AA amyloid secondary to familial Mediterranean fever / TRAPS (Hibernian fever) - no histology Other Familial AA amyloid secondary to familial Mediterranean fever / TRAPS (Hibernian fever) - histologically proven Other Myeloma kidney - no histology Other Myeloma cast nephropathy - histologically proven Other Light chain deposition disease Other Immunotactoid / fibrillary nephropathy Other Haemolytic uraemic syndrome (HUS) - diarrhoea associated Other Atypical haemolytic uraemic syndrome (HUS) - diarrhoea negative Other Thrombotic thrombocytopenic purpura (TTP) Other Haemolytic uraemic syndrome (HUS) secondary to systemic disease Other Congenital haemolytic uraemic syndrome (HUS) Other Familial haemolytic uraemic syndrome (HUS) Other Familial thrombotic thrombocytopenic purpura (TTP) Other Nephropathy due to pre-eclampsia / eclampsia Other Sickle cell nephropathy - no histology Other Sickle cell nephropathy - histologically proven Other Kidney tumour Other Renal cell carcinoma - histologically proven Other Transitional cell carcinoma - histologically proven Other Wilms tumour - histologically proven Other Mesoblastic nephroma - histologically proven Other / 7

7 3517 Single kidney identified in adulthood Other Chronic kidney disease (CKD) / chronic renal failure (CRF) caused by tumour nephrectomy Other Chronic kidney disease (CKD) / chronic renal failure (CRF) due to traumatic loss of kidney Other Chronic kidney disease (CKD) / chronic renal failure (CRF) due to donor nephrectomy Other Haematuria and proteinuria - no histology Other AND Chronic renal failure due to systemic infection Other Isolated haematuria - no histology Other Isolated proteinuria - no histology Other Acute kidney injury Acute Renal Failure Acute kidney injury due to hypovolaemia Acute Renal Failure Acute kidney injury due to circulatory failure Acute Renal Failure Acute kidney injury due to sepsis Acute Renal Failure Acute kidney injury due to rhabdomyolysis Acute Renal Failure Acute kidney injury due to nephrotoxicity Acute Renal Failure Acute cortical necrosis Acute Renal Failure Acute pyelonephritis Acute Renal Failure Cardiorenal syndrome Cardiorenal syndrome Chronic kidney disease (CKD) / chronic renal failure (CRF) - aetiology uncertain / unknown - no histology Unknown Chronic kidney disease (CKD) / chronic renal failure (CRF) - aetiology uncertain / unknown - histologically proven Unknown Renal failure Unknown Chronic renal failure Unknown / 7