(for PKU see pages 11-13) + Description A food for special medical purposes. Cooler is a ready-to-drink protein substitute containing essential and non-essential amino acids (but excluding the offending amino acids(s)), carbohydrate, vitamins, minerals, trace elements and the Omega-3 long chain polyunsaturated fatty acids (LCPs); Docosahexaenoic acid (DHA) and Eicosapentaenoic acid (EPA). Contains sugar and sweeteners. Product Indication Free From Flavour options Maple Syrup Urine Disease Leucine, Isoleucine and Valine and Orange Homocystinuria Methionine and Orange Tyrosinaemia Phenylalanine and Tyrosine and Orange Methylmalonic Acidaemia / Propionic Acidaemia Methionine, Threonine and Valine. Low Isoleucine. Isovaleric Acidaemia and other disorders requiring Leucine-free protein substitutes Leucine
MSUD HCU Tyrosinaemia MMA/PA IVA Age Range Suitable from 3 years of age. 1. The daily protein requirement is given as. 2. Additional protein is provided from exchanges of natural protein, to provide restricted amino acids in controlled amounts, which is essential for growth and development. 3. Foods high in carbohydrate and fat, but low in protein, should be provided to supply the remainder of the energy. Dosage and Administration To be determined by the clinician or dietitian, and is dependent on the age, body weight and medical condition of the patient. = 15g PE = 10g PE = 20g PE Preparation Guidelines 1. Shake well 2. Open Water or mitted drinks should be taken after the. 3. Drink
Important NOTICE Must only be given to patients under strict medical suvision. is for the dietary management of maple syrup urine disease. is for the dietary management of homocystinuria. is for the dietary management of tyrosinaemia. is for the dietary management of Methylmalonic Acidaemia and Propionic Acidaemia. Nutritional Information * Figures in brackets represent MMA/PA and IVA s Nutritional Information is for the dietary management of Isovaleric acidaemia and other disorders requiring leucine free protein substitute. Suitable from 3 years of age. Diet must be supplemented with natural protein, water and other nutrients in prescribed quantities to supply additional nutritional requirements. Not for use as a sole source of nutrition. For enteral use only. 100ml Cooler10 Cooler15 Cooler20 Energy kj 302 261 393 526 (331)* (430)* kcal 71 62 92 124 (79)* (103)* Protein equivalent g 11.5 10 15 20 Carbohydrate g 5.4 4.7 7.0 9.4 of which sugars g 4.5 3.9 5.9 7.8 Fat g 0.4 0.3 0.5 0.7 (1.3)* (1.7)* of which saturates g 0.10 0.09 0.13 0.17 (0.25)* (0.33)* of which DHA mg 77 67 100 134 of which EPA mg 18 16 23 31 Fibre g 0 0 0 0
100ml Cooler10 Cooler15 Cooler20 Vitamins Vitamin A µg RE 160 139 208 278 IU 533 464 693 926 Vitamin D μg 5.8 5.0 7.5 10 IU 232 202 300 400 Vitamin E mg α TE 3.0 2.6 3.9 5.2 IU 4.5 3.9 5.8 7.7 Vitamin C mg 21 18 27 36 Vitamin K μg 19 17 25 34 Thiamin mg 0.40 0.38 0.50 0.70 Riboflavin mg 0.44 0.38 0.57 0.77 Niacin mg 4.8 4.2 6.2 8.4 Niacin equivalent MSUD mg 12.3 10.7 16 21.4 HCU mg 10.1 8.8 13.2 17.6 TYR mg 10.3 9.0 13.4 17.9 MMA/PA mg 9.1 11.8 IVA mg 9.1 11.8 Vitamin B6 mg 0.50 0.4 0.70 0.9 Folic acid μg 77 67 100 134 Vitamin B12 μg 0.90 0.80 1.2 1.6 Biotin μg 36 31 47 63 Pantothenic acid mg 1.5 1.3 2.0 2.6 Choline mg 115 100 150 201 Myo-Inositol mg 0 0 0 0 Minerals Sodium mg 98 85 127 171 mmol 4.2 3.7 5.5 7.3 Potassium mg 181 157 235 315 mmol 4.5 3.9 5.9 7.9 Chloride mg 140 122 182 244 mmol 3.9 3.4 5.1 6.8 Calcium mg 230 200 299 400 mmol 5.8 5.0 7.5 10 Phosphorus mg 205 178 267 357 mmol 6.6 5.7 8.4 11.4 Magnesium mg 72 63 94 125 mmol 3.0 2.6 3.9 5.2 Trace Elements Iron mg 4.2 3.7 5.4 7.3 Cop µg 420 365 546 731 Zinc mg 4.2 3.7 5.4 7.3 Manganese mg 0.60 0.50 0.80 1.0 Iodine μg 49 43 63 84 Molybdenum μg 28 24 36 48 Selenium μg 17 15 22 29 Chromium μg 17 15 22 29
Amino Acids 100ml MSUD L-Alanine g 1.57 0.61 0.93 1.29 1.34 L-Arginine g 1.49 1.01 1.14 1.33 1.27 L-Aspartic acid g 1.88 1.35 1.76 2.31 1.61 L-Cystine g 0.44 0.41 0.42 0.56 0.38 L-Glutamine g 0.00 0.00 0.00 0.00 0.00 Glycine g 1.25 0.89 0.93 0.61 1.07 L-Histidine g 0.53 0.64 0.62 0.87 0.46 L-Isoleucine g 0.00 0.95 1.03 0.04 0.93 L-Leucine g 0.00 1.65 1.66 1.82 0.00 L-Lysine g 1.12 1.07 1.18 1.42 0.96 L-Methionine g 0.32 0.00 0.27 0.00 0.28 L-Phenylalanine g 0.84 0.74 0.00 0.87 0.72 L-Proline g 1.32 0.93 0.95 0.64 1.13 L-Serine g 0.89 0.71 0.73 0.96 0.76 L-Threonine g 0.80 0.73 0.80 0.00 0.69 L-Tryptophan g 0.45 0.32 0.33 0.36 0.38 L-Tyrosine g 0.89 0.73 0.00 0.87 0.76 L-Valine g 0.00 1.05 1.13 0.00 1.23 L-Carnitine mg 13 13 13 13 13 Taurine mg 25 25 25 25 25 Osmolality MSUD, HCU and TYR s = 1900 mosm/kg MMA/PA = 1650 mosm/kg IVA = 1740 mosm/kg Allergen Declaration Contains oil derived from fish sources, milk and soya lecithin. Storage Store in a cool, dry place and refrigerate before use if desired. Once open drink immediately or refrigerate and use within 24 hours. HCU TYR MMA/PA Pack size/volume 30 x pouches = 2.61L. 30 x pouches = 3.9L. 30 x pouches = 5.22L. Shelf life 9 months. IVA MSUD HCU TYR MMA/PA IVA