Idiopathic dilatation of the pulmonary artery : radiographic and MDCT features in 6 cases Poster No.: P-0075 Congress: ESTI 2014 Type: Authors: Educational Poster J. J. Woo 1, K. Y. Lee 2, Y. Cho 1, J. K. An 1, D. J. Kim 1 ; 1 Seoul/KR, 2 Ansan/KR Keywords: DOI: Congenital, Aneurysms, Computer Applications-3D, CT-High Resolution, CT-Angiography, Conventional radiography, Lung, Cardiovascular system 10.1594/esti2014/P-0075 Any information contained in this pdf file is automatically generated from digital material submitted to EPOS by third parties in the form of scientific presentations. References to any names, marks, products, or services of third parties or hypertext links to thirdparty sites or information are provided solely as a convenience to you and do not in any way constitute or imply ECR's endorsement, sponsorship or recommendation of the third party, information, product or service. ECR is not responsible for the content of these pages and does not make any representations regarding the content or accuracy of material in this file. As per copyright regulations, any unauthorised use of the material or parts thereof as well as commercial reproduction or multiple distribution by any traditional or electronically based reproduction/publication method ist strictly prohibited. You agree to defend, indemnify, and hold ECR harmless from and against any and all claims, damages, costs, and expenses, including attorneys' fees, arising from or related to your use of these pages. Please note: Links to movies, ppt slideshows and any other multimedia files are not available in the pdf version of presentations. www.myesr.org Page 1 of 7
Learning objectives To retrospectively review imaging findings and clinical implications of idiopathic dilatation of the pulmonary artery to improve understanding and recognition of this rare entity. Background Definition of idiopathic pulmonary artery dilatation Focal dilatation of the main pulmonary art. with or without dilatation of the right and left pulmonary art. (main PA >29mm, right interlobar art. >17mm on CT) Without an identifiable cause - Exclusion of other causes of a dilated pulmonary artery : pulmonary hypertension, tricuspid valve disease, pulmonary valve stenosis, congenital heart diseases, syphilis, Behcet's disease, atherosclerosis, trauma, connective tissue etc. Rare anomaly with poorly understood pathogenesis Materials Six patients with idiopathic dilatation of the pulmonary artery were included after searching the radiology database at a large teaching hospital. The radiograph, MDCT images and clinical manifestation were reviewed. Imaging findings OR Procedure details Sex Age Diameter of PA Ratio of PA/aorta Right PA(mm) Patient 1 F 16 29 mm 29/23 13 12 Left PA(mm) Patient 2 F 26 34 mm 34/26 13.5 16.8 Patient 3 F 28 43 mm 43/25 20 23.6 Page 2 of 7
Patient 4 F 47 39 mm 39/30 20.9 22.2 Patient 5 M 54 35 mm 35/32 17 30 Patient 6 M 59 32 mm 32/30 18 34 Images for this section: Fig. 1: 28-year-old woman with negative symptom. A. Posteroanterior chest radiograph shows left hilar bulging opacity (white arrow). Page 3 of 7
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Conclusion Radiologists should be aware of the definition and imaging findings of the idiopathic dilatation of the pulmonary artery. Idiopathic pulmonary artery dilatation should be included in the differential diagnosis when prominent pulmonary conus or left hilar bulging opacity without any other findings of pulmonary hypertension is present on chest radiograph. Pulmonary CT angiography may be the gold standard for the diagnosis of the idiopathic pulmonary artery dilatation. References Nguyen ET, Silva CI, Seely JM, Chong S, Lee KS, Müller NL. Pulmonary artery aneurysms and pseudoaneurysms in adults: findings at CT and radiography. Am J Roentgenol. 2007;188:W126-34. Subrato J. Deb, Kenton J. Zehr, Raymond C. Shields, Idiopathic Pulmonary Artery Aneurysm. Ann Thorac Surg 2005;80:1500-2. Orman G, Guvenc TS, Balci B, Duymus M, Sevingil T. Idiopath#c pulmonary artery aneurysm. Ann Thorac Surg 2013;95:e33-4. Ring NJ, Marshall AJ, Idiopathic dilatation of the pulmonary artery. Br J Radiol. 2002;75:532-5. Personal Information Jeong Joo Woo1, Ki Yeol Lee2, Young Kwon Cho1, Jin Kyung An1, Dae Jung Kim1 1Department of Radiology, Eulji University College of Medicine, Eulji Hospital, Seoul, Korea 2Department of Radiology, Korea University Ansan Hospital, Ansan, Korea Page 6 of 7
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