STVARI, KI JIH MORA NEFROLOG VEDETI O REVMATOLOGIJI. Vesna Kovačič Grobelšek Odd. Za revmatologijo UKC Maribor

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1 STVARI, KI JIH MORA NEFROLOG VEDETI O REVMATOLOGIJI Vesna Kovačič Grobelšek Odd. Za revmatologijo UKC Maribor

2 Revmatološke in ledvične bolezni 18% bolnikov v revmatološki ambulano ima znižano glomerulno filtracijo pod 60 ml/min V splošni populaciji okoli 5% (1) 1. Hill AJ, Thomson RJ, Hunter JA, Traynor JP: The prevalence of chronic kidney disease in rheumatology outpaoents. Sco_ Med J 2009, 54:9-12

3 Ko se srečamo z bolnikom, ki ima revmatološko bolezen in sočasno ledvično bolezen se je potrebno vprašao 1. Ali je ledvična bolezen posledica revmatološke bolezni? 2. Ali je ledvična bolezen povezana z zdravljenjem revmatološke bolezni? 3. Ali je revmatološka bolezen posledica ledvične bolezni? 4. Ali gre za sistemsko bolezen?

4 1. Ali je ledvična bolezen zaplet revmatološke bolezni? Anders HJ, Vielhauer V, Renal co- morbidity in paoent with rheumaoc diseases. ArthriOs Res Ther Jun 29;13(3):222

5 REVMATOIDNI ARTRITIS kronična, sistemska vnetna bolezen prizadene sklepe MATRIX študija bolnikov 19% bolnikov z RA je imelo povišan kreaonin Proteinurija je bila prisotna pri 16%, hematurija pri 17% 1. Karie S, Gandjbakhch F, Janus N, Launay-Vacher V, Rozenberg S, Mai Ba CU, Bourgeois P, Deray G: Kidney disease in RA patients: prevalence and implication on RA-related drugs management: the MATRIX study..rheumatology (Oxford) 2008, 47:

6 REVMATOIDNI ARTRITIS LEDVIČNA PRIZADETOST Biopsijski vzorci 110 bolnikov 4 36% mezangijski GN Povezan z RA, povezava z višjimi Otri RF 4% fokalno proliferaovni GN 3% minimal- change GN 1% Akutni intersocijski nefrios 30% amiloidoza 17% membranozni GN PreparaO zlata AnO TNF alfa (etanercept, adalimumab) 3. Myllykangas- Luosujarvi R, Aho K, KauOainen H, Hakala M: Amyloidosis in a nadonwide series of 1666 subjects with rheumatoid arthrids who died during 1989 in Finland. Rheumatology (Oxford) 1999, 38: Helin HJ, Korpela MM, Mustonen JT, Pasternack AI: Renal biopsy findings and clinicopathologic correladons in rheumatoid arthrids. Arthri6s Rheum 1995, 38:

7 SISTEMSKA SKLEROZA okluzivna vaskulopaoja s fibroziranjem visceralno in žilno sklerodermično spremenjena koža LEDVIČNA KRIZA 2 do 15% bolnikov maligna hipertenzija z akutno ledvično odpovedjo 10% normotenzivnih!! levostranskim srčnim popuščanjem mikroangiopaočno hemoliočno anemijo in trombocitopenijo

8 SISTEMSKA SKLEROZA Dejavniki tveganja Hitro napredujoča difuzna oblika Ssc zdravljenje z glukokorokoidi v visokih odmerkih prisotnost ano- RNA polimeraza III, drobno grudasta (S+) ANA Mouthon L, Berezne A, Scleroderma renal crisis: a rare but severe complication of systemic sclerosis.clin Rev Allergy Immunol 2011 Apr;40(2):84-91

9 SJÖGRENOV SINDROM Polklonalna akovacija B- limfocitov z infiltracijo žlez z zunanjim izločanjem Suho oko, suha usta Kohorta 715 bolnikov 4 Prizadetost ledvic okoli 5% 37% TUBULOINTERSTICIJSKI NEFRITIS Distalna (tip I) ledvična tubulna acidoza (RTA) 5% popolna, 25% nepopolna 1 48% GLOMERULNEFRITIS Krioglobulinemični membrano- proliferaovni GN(IgM, C3) 14% TIN in GN SSA/Ro, SSB/La, revma faktor in hipergamaglobulinemija je bila prisotna pri vseh bolnikih z ledvično prizadetostjo 2 Pri vseh bolnikih z distalno RTA so bila poziovna proojedrna prootelesa (ANA) in pri 85.7% bodisi SSA ali SSB 3 GN Slabša prognoza razvoj limfoma 1. Both T, Prevalence of distal renal tubular acidosis in primary Sjogren s sindrome, Rheumatology 2014 Oct 29 epub ahead of print 2. Maripuri S, Grande JP, Osborn TG, Fervenza FC, Matteson EL, Donadio JV, Hogan MC: Renal involvement in primary Sjogren's syndrome: a clinicopathologic study. Clin J Am Soc Nephrol 2009, 4: Aasarod K, Haga HJ, Berg KJ, Hammerstrom J, Jorstad S: Renal involvement in primary Sjogren's syndrome. QJM 2000, 93:

10 DERMATOMIOZITIS in POLIMIOZITIS Mišice počasi napredujoča, simetrična slabost proksimalnih mišic Kožne spremembe Go_ronove papule heliotropni eritem RABDOMIOLIZA Akutna tubulna nekroza GLOMERULONEFRITIS PM MezangioproliferaOvni GN membranska nefropatija Crescendo GN s FSGS DM membranska nefropaoja

11 SPONDILOARTRITISI skupina bolezni klinična slika hrbtenica periferni sklepi entezios zunajsklepna prizadetost dober učinek NSAR Ledvična prizadetost 35% bolnikov z AS povišan kreaonin ali patološki sediment IgA nefropaoja ali amiloidoza 5 z zdravili povzročena nefrotoksičnost IntersOcijski nefrios Z NSAR povzročen membranozni GN 5. Vilar MJ, Cury SE, Ferraz MB, Sesso R, Atra E: Renal abnormalioes in ankylosing spondylios. Scand J Rheumatol 1997, 26:19-23

12 Ko se srečamo z bolnikom, ki ima revmatološko bolezen in sočasno ledvično bolezen se je potrebno vprašao 1. Ali je ledvična bolezen posledica revmatološke bolezni? 2. Ali je ledvična bolezen povezana z zdravljenjem revmatološke bolezni? 3. Ali je revmatološka bolezen posledica ledvične bolezni? 4. Ali gre za sistemsko bolezen?

13 2. Ali je ledvična bolezen povezana z zdravljenjem revmatološke bolezni? NSAR Imunomodulirajoča zdravila Biološka zdravila

14 NSAR in ledvična bolezen Pri 1-5% bolnikov, ki uporabljajo NSAR Povečano tveganje kronična ledvična bolezen starejši dehidracija Bruhanje/driska SepOčna stanja Krvavitve srčno popuščanje jetrna ciroza nefrotski sindrom hiperkalcemija sočasna raba zdravil DiureOki ACE inhibitorji Angiotenzin receptor blokatorji Kalcinevrinski inhibitorji Blokirajo vazodilatatorni učinek prostaglandinov na aferentno arteriolo Zmanjšajo glomerulno filtracijo

15 Akutna ledvična odpoved Akutni intersocijski nefrios Nefrotski sindrom Minimal change disease Membranska nefropaoja Hiponatriemija Hiperkaliemija (Op 4 renalna tubulna acidoza) Hipertenzija/edemi Akutna papilarna nekroza Kronični tubolintersocijski nefrios/analgeočna nefropaoja Uroepitelni malignomi

16 Imunomodulatorna zdravila Ciklosporin, preparao zlata in D- penicilamin Nefrotoksični Metotrexate Ni nefrotoksičen 80-90% se izloča preko ledvic Zmanjšano izločanje pri KLB poveča neledvično toksičnost AnOmalariki, leflunomid, sulfasalazin, azaooprin Delno izločanje preko ledvic Če GFR <50 ml/minuto je potrebno odmerek znižao

17 Swarup A, Sachdeca N, Dosing of anorheumeoc drugs in renal disease and dialysis, J Clin Rheumatol 2004; 10:

18 Ko se srečamo z bolnikom, ki ima revmatološko bolezen in sočasno ledvično bolezen se je potrebno vprašao 1. Ali je ledvična bolezen posledica revmatološke bolezni? 2. Ali je ledvična bolezen povezana z zdravljenjem revmatološke bolezni? 3. Ali je revmatološka bolezen posledica ledvične bolezni? 4. Ali gre za sistemsko bolezen?

19 3. Ali je revmatološka bolezen posledica ledvične bolezni ali njenega zdravljenja? spremembe v ravnovesju fosfata, kalcija in vitamina D privede do hiperfosfatemije in hipokalcemije sekundarni hiperparaoroidizem Izvenkostne kalcifikacije PeriarOkularni depozio kalcija hondrokalcinoza in precipitacije kristalov kalcijevega pirofosfat dihidrata - pseudoproon Hiperurikemija zmanjšan klirens urata pri ledvični bolezni Hiperurikemija uratna nefropaoja - KLB

20 PROTIN Pri KLB problemaočno zdravljenje Akutni napad NSAR se izogibamo Kolhicin ima ozko terapevtsko okno izogibamo GlukokorOkoidi kratkotrajno Vzdrževalna terapija Alopurinol potrebno prilagodio odmerek Febuxostat varen pri GFR >30 ml/minute/1.73 m 2

21 Ko se srečamo z bolnikom, ki ima revmatološko bolezen in sočasno ledvično bolezen se je potrebno vprašao 1. Ali je ledvična bolezen posledica revmatološke bolezni? 2. Ali je ledvična bolezen povezana z zdravljenjem revmatološke bolezni? 3. Ali je revmatološka bolezen posledica ledvične bolezni? 4. Ali gre za sistemsko bolezen?

22 4. Ali gre za sistemsko bolezen? KO DOKAŽEMO ledvično prizadetost vedno AKTIVNO iščemo prizadetost drugih organskih sistemov Usmerjena vprašanja

23 1. KOŽA, SLUZNICE in OČI Ali opažate kožni izpuščaj? Ali na soncu dobite rdeč in srbeč izpuščaj?

24 Ali vam čezmerno izpadajo lasje? Ali vam na mrazu pobledijo prs6 na rokah? Ali ste spontano splavili ali rodili mrtvorojenega otroka? Ali opažate razjede na sluznicah ust, nosu, spolovila?

25 Ali vas sklepi bolijo/otekajo? Ali ste preboleli vnetje oči? konjunkovios uveios sklerios in episklerios Ali imate pogosto občutek suhih ust in oči?

26 ZGORNJA in SPODNJA DIHALA Ali imate razjede/ krvavkast izcedek iz nosu? Ali imate bolečino v paranazalnih sinusih? Ali imate težave s sluhom ali hripavost? Ali kašljate in izkašljujete? Ali opažate bolečino ob dihanju? Ali se zadihate ob naporu? Imate astmo?

27 SRCE in OŽILJE Anamneza klavdikacijske bolečine v okončinah? Ali imate bolečine za prsnico, zadihanost ob naporu?

28 TREBUH Imate bolečine v trebuhu? Ste opazili krvave driske? ŽIVČEVJE Ali opažate glavobole, osebnostno spremenjenost, zmedenost/pozabljivost? Ali imate epilep6čne napade? Ali ste utrpeli ICV? Ali opažate mravljinčenje, pekoč občutek ali gluhost udov?

29

30 Ko se srečamo z bolnikom, ki ima revmatološko bolezen in sočasno ledvično bolezen se je potrebno vprašao 1. Ali je ledvična bolezen posledica revmatološke bolezni? 2. Ali je ledvična bolezen povezana z zdravljenjem revmatološke bolezni? 3. Ali je revmatološka bolezen posledica ledvične bolezni? 4. Ali gre za sistemsko bolezen?

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