Two Cases of Benign Monomelic Amyotrophy of the Lower Extremities

Transcription

1 Journal of the K. S. C. N. Vol. 2, No. 2 Two Cases of Benign Monomelic Amyotrophy of the Lower Extremities Dong Kuck Lee, M.D. Department of Neurology, School of Medicine, Catholic University of Daegu - Abstract - Benign monomelic amyotrophy(bma) is an uncommon cause of progressive mildly disabling atrophy and weakness of a limb. It predominantly affects the distal upper limb of young men. I present two men with BMA of the lower extremities. Although the disorder seemed clinically confined to a arm or leg, I confirmed by electromyography evidence of denervation in the other extremities. I reviewed the literatures and discuss the differential diagnosis. BMA is a diagnosis of exclusion that requires consideration in men with unilateral arm or leg atrophy and weakness. Key Words : Benign monomelic amytrophy CASE REPORTS Case No

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3 Table 1. Monomelic amyotrophy synonyms 5 Monomelic atrophy Benign focal atrophy Benign focal amyotrophy Benign monomelic amyotrophy Distal amyotrophy of predominantly the upper limbs Juvenile segmental muscular atrophy Juvenile type of distal and segmental atrophy of upper extremities Juvenile muscular atrophy of the upper extremity Juvenile nonprogressive muscular atrophy localized in hand and forearm Juvenile distal spinal muscular atrophy of upper extremities Juvenile amyotrophy of distal upper extremity Non-familial spinal segmental muscular atrophy in juvenile and young subjects Non-familial juvenile distal spinal muscular atrophy of upper extremity Non-familial juvenile central neurogenic muscular atrophy Focal cervical poliopathy causing juvenile muscular atrophy of distal upper extremity Monomelic spinal muscular atrophy Benign juvenile focal muscular atrophy of upper extremities Spinal monomelic amyotrophy Unilateral juvenile muscular atrophy of upper limbs 127

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